Síndrome de Sjögren

  1. Pijoan Moratalla, C.M. 1
  2. Blanco Cáceres, B.A. 1
  3. Revenga Martínez, M. 2
  4. Loarce Martos, J. 1
  5. Morell Hita, J.L. 1
  1. 1 Servicio de Reumatología. Instituto Ramón y Cajal de Investigación Sanitaria (IRYCIS). Hospital Universitario Ramón y Cajal, Madrid, España
  2. 2 Servicio de Reumatología. Instituto Ramón y Cajal de Investigación Sanitaria (IRYCIS). Hospital Universitario Ramón y Cajal, Madrid, España Departamento de Medicina y Especialidades Médicas. Universidad de Alcalá. Alcalá de Henares, Madrid, España
Revista:
Medicine: Programa de Formación Médica Continuada Acreditado

ISSN: 0304-5412

Año de publicación: 2021

Serie: 13

Número: 30

Páginas: 1694-1701

Tipo: Artículo

DOI: 10.1016/J.MED.2021.03.029 DIALNET GOOGLE SCHOLAR

Otras publicaciones en: Medicine: Programa de Formación Médica Continuada Acreditado

Objetivos de desarrollo sostenible

Resumen

Sjögren's syndrome (SS) is a chronic autoimmune disease characterized by infiltration and progressive destruction of the exocrine glands. It can appear primarily or associated with other autoimmune diseases. It is characterized by intense xerophthalmia and xerostomia but extraglandular disease can also develop, most commonly affecting joints, lungs, kidneys or the nervous system, generally conditioning both more aggressive treatments and poorer prognosis. Diagnosis includes confirmation of glandular hyposecretion by different techniques and the presence of anti-Ro/SSA or anti-La/SSB autoantibodies. Treatment includes symptomatic management of dryness and the prevention of the potential complications that this entails and secondly immunosuppressive and biologic drugs and to help control extraglandular disease, which confers a worse long-term prognosis.

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Fuente de los datos: Dialnet