Síndrome de aorta media congénito en la edad adulta. A propósito de un caso

  1. Molina Borao, Isabel 1
  2. Álvarez Fuente, María 1
  3. Centella Hernández, Tomasa 2
  4. Martín Pinacho, Jesús Javier 3
  5. Sánchez Pérez, Inmaculada 1
  6. Rivero Jiménez, Natalia 1
  7. del Cerro Marín, Maria Jesus 1
  1. 1 Servicio de Cardiología Pediátrica y Cardiopatías Congénitas. Hospital Universitario Ramón y Cajal. Madrid. España
  2. 2 Servicio de Cirugía Cardiaca Infantil y Cardiopatías Congénitas. Hospital Universitario Ramón y Cajal. Madrid. España
  3. 3 Servicio de Radiología. Hospital Universitario Ramón y Cajal. Madrid. España
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Journal:
Revista de Ecocardiografía práctica y otras Técnicas de Imagen Cardíaca (RETIC)

ISSN: 2529-976X

Year of publication: 2023

Issue Title: Journal of Practical Echocardiography and Other Cardiac Imaging Techniques

Volume: 6

Issue: 1

Pages: 22-25

Type: Article

DOI: 10.37615/RETIC.V6N1A4 DIALNET GOOGLE SCHOLAR lock_openOpen access editor

More publications in: Revista de Ecocardiografía práctica y otras Técnicas de Imagen Cardíaca (RETIC)

Abstract

We present the case of a 35-year-old patient with a diagnosis of congenital middle aortic syndrome corrected in childhood with aortic bypass interposition of a Dacron conduit. During follow-up, she was diagnosed with arterial hypertension, for which antihypertensive treatment was started and a stent was implanted in the conduit. A control CT of the aorta revealed a rib lesion suggestive of osteochondroma that compressed the duct. Cardiac catheterization confirmed hemodynamic stenosis due to extrinsic compression of the rib lesion at the level of the previously implanted stent. The CT imaging study helped to diagnose a complication at the level of the aorta that was  undetected in other imaging techniques.

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